Dermatofibrosarcoma protuberans in adolescence: a case report and literature review
Clinical Practice
Agnietė Valiulytė
Milda Gudavičiūtė
Kęstutis Trainavičius
Dmitrij Šeinin
Published 2015-03-31
https://doi.org/10.15388/LietChirur.2015.1.5333
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Keywords

dermatofibrosarcoma protuberans in children
soft tissue sarcomas
fibrosarcomous transformation
surgical treatment

How to Cite

1.
Valiulytė A, Gudavičiūtė M, Trainavičius K, Šeinin D. Dermatofibrosarcoma protuberans in adolescence: a case report and literature review. LS [Internet]. 2015Mar.31 [cited 2022Sep.26];14(1):61-4. Available from: https://www.journals.vu.lt/lietuvos-chirurgija/article/view/5333

Abstract

Dermatofibrosarcoma protuberans is a very rare malignant neoplasm in children. It is reported that the classic form of dermatofibrosarcoma has a very limited metastatic potential, while a fibrosarcomous transformation of dermatofibrosarcoma protuberans has a much higher potential. We present a case of a 17-year-old boy with a huge ulcerated mass (17 x 15 cm) on his right thigh. At operation, the pathological diagnosis was dermatofibrosarcoma protuberans with a fibrosarcomous component. All lesions were removed by surgical excision with a margin of 1.5 to 3 cm. After one year, there is no evidence of tumor recurrence.

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