Surgical management of adult Hirschsprung’s disease by subtotal colectomy: a possible alternative
Clinical Practice
Edvinas Kildušis
Tomas Poškus
Kęstutis Strupas
Published 2016-12-22
https://doi.org/10.15388/LietChirur.2016.4.10280
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Keywords

adult Hirschsprung’s disease
constipation
megacolon
aganglionosis

How to Cite

1.
Kildušis E, Poškus T, Strupas K. Surgical management of adult Hirschsprung’s disease by subtotal colectomy: a possible alternative. LS [Internet]. 2016Dec.22 [cited 2022Oct.7];15(4):162-4. Available from: https://www.journals.vu.lt/lietuvos-chirurgija/article/view/10280

Abstract

Adult Hirschsprung’s disease (AHD) is a rare and often undiagnosed condition. At present, only a limited number of cases have been reported. We managed a 19-year-old woman with rich history of chronic constipation and abdominal discomfort. Abdominal radiography and barium enema examination demonstrated massively dilated colon (up to 15 cm in diameter). Full-thickness rectal biopsy showed absence of ganglionic cells. AHD was diagnosed and subtotal colectomy with ileorectal anastomosis was performed. At five-year follow up, the patient had significantly improved defecation and quality of life and was extremely satisfied with the operation. AHD should be considered in patients with long-standing and refractory constipation with megacolon. We advocate a subtotal colectomy with ileorectal anastomosis as one of the possible surgical alternatives in such young patients.

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