Surgical management of adult Hirschsprung’s disease by subtotal colectomy: a possible alternative
Clinical Practice
Edvinas Kildušis
Tomas Poškus
Kęstutis Strupas
Published 2016-12-22
https://doi.org/10.15388/LietChirur.2016.4.10280
PDF (Lithuanian)

Keywords

adult Hirschsprung’s disease
constipation
megacolon
aganglionosis

How to Cite

1.
Kildušis E, Poškus T, Strupas K. Surgical management of adult Hirschsprung’s disease by subtotal colectomy: a possible alternative. LS [Internet]. 2016 Dec. 22 [cited 2024 Mar. 29];15(4):162-4. Available from: https://www.journals.vu.lt/lietuvos-chirurgija/article/view/10280

Abstract

Adult Hirschsprung’s disease (AHD) is a rare and often undiagnosed condition. At present, only a limited number of cases have been reported. We managed a 19-year-old woman with rich history of chronic constipation and abdominal discomfort. Abdominal radiography and barium enema examination demonstrated massively dilated colon (up to 15 cm in diameter). Full-thickness rectal biopsy showed absence of ganglionic cells. AHD was diagnosed and subtotal colectomy with ileorectal anastomosis was performed. At five-year follow up, the patient had significantly improved defecation and quality of life and was extremely satisfied with the operation. AHD should be considered in patients with long-standing and refractory constipation with megacolon. We advocate a subtotal colectomy with ileorectal anastomosis as one of the possible surgical alternatives in such young patients.

PDF (Lithuanian)

Downloads

Download data is not yet available.

Most read articles by the same author(s)

<< < 1 2 3 4 5 > >>